Human Gene DECR1 (ENST00000220764.7_10) from GENCODE V47lift37
Description: 2,4-dienoyl-CoA reductase 1, transcript variant 1 (from RefSeq NM_001359.2)
Gencode Transcript: ENST00000220764.7_10
Gencode Gene: ENSG00000104325.7_15
Transcript (Including UTRs)
Position: hg19 chr8:91,013,705-91,065,861 Size: 52,157 Total Exon Count: 10 Strand: +
Coding Region
Position: hg19 chr8:91,013,721-91,064,125 Size: 50,405 Coding Exon Count: 10
Data last updated at UCSC: 2024-08-22 23:36:26
Sequence and Links to Tools and Databases
Comments and Description Text from UniProtKB
ID: DECR_HUMAN
DESCRIPTION: RecName: Full=2,4-dienoyl-CoA reductase, mitochondrial; EC=1.3.1.34; AltName: Full=2,4-dienoyl-CoA reductase [NADPH]; Short=4-enoyl-CoA reductase [NADPH]; Flags: Precursor;
FUNCTION: Auxiliary enzyme of beta-oxidation. It participates in the metabolism of unsaturated fatty enoyl-CoA esters having double bonds in both even- and odd-numbered positions. Catalyzes the NADP-dependent reduction of 2,4-dienoyl-CoA to yield trans-3- enoyl-CoA.CATALYTIC ACTIVITY: Trans-2,3-didehydroacyl-CoA + NADP(+) = trans,trans-2,3,4,5-tetradehydroacyl-CoA + NADPH.BIOPHYSICOCHEMICAL PROPERTIES: Kinetic parameters: KM=7.7 uM for NADPH; KM=14.3 uM for trans-2,trans-4-hexadienoyl-CoA; Vmax=30.3 umol/min/mg enzyme;SUBUNIT: Homotetramer.SUBCELLULAR LOCATION: Mitochondrion.TISSUE SPECIFICITY: Heart = liver = pancreas > kidney >> skeletal muscle = lung.SIMILARITY: Belongs to the short-chain dehydrogenases/reductases (SDR) family. 2,4-dienoyl-CoA reductase subfamily.WEB RESOURCE: Name=GeneReviews; URL="http://www.ncbi.nlm.nih.gov/sites/GeneTests/lab/gene/DECR1";
Primer design for this transcript
MalaCards Disease Associations
MalaCards Gene Search: DECR1
Diseases sorted by gene-association score: 2,4-dienoyl-coa reductase deficiency * (78), hyperlysinemia (12), chronic granulomatous disease (4), suppurative lymphadenitis (1), retinitis pigmentosa 47 (1), parasitic protozoa infectious disease (1), adrenal cortical adenocarcinoma (1), trichosporonosis (1), image syndrome (1), periodontosis (1), d-2-hydroxyglutaric aciduria (1), vulvitis (1), neurodermatitis (1)* = Manually curated disease association
Comparative Toxicogenomics Database (CTD)
Common Gene Haplotype Alleles
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RNA-Seq Expression Data from GTEx (53 Tissues, 570 Donors)
Microarray Expression Data
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mRNA Secondary Structure of 3' and 5' UTRs
The RNAfold program from the Vienna RNA Package is used to perform the secondary structure predictions and folding calculations. The estimated folding energy is in kcal/mol. The more negative the energy, the more secondary structure the RNA is likely to have.
Protein Domain and Structure Information
InterPro Domains: Graphical view of domain structure IPR002347 - Glc/ribitol_DH
IPR016040 - NAD(P)-bd_dom
Pfam Domains: PF00106 - short chain dehydrogenase
PF08659 - KR domain
PF13561 - Enoyl-(Acyl carrier protein) reductase
SCOP Domains: 51735 - NAD(P)-binding Rossmann-fold domains
Protein Data Bank (PDB) 3-D Structure MuPIT help
ModBase Predicted Comparative 3D Structure on Q16698
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Orthologous Genes in Other Species
Orthologies between human, mouse, and rat are computed by taking the best BLASTP hit, and filtering out non-syntenic hits. For more distant species reciprocal-best BLASTP hits are used. Note that the absence of an ortholog in the table below may reflect incomplete annotations in the other species rather than a true absence of the orthologous gene.
Gene Ontology (GO) Annotations with Structured Vocabulary
Descriptions from all associated GenBank mRNAs
BC105080 - Homo sapiens 2,4-dienoyl CoA reductase 1, mitochondrial, mRNA (cDNA clone MGC:132740 IMAGE:8144083), complete cds.BC105082 - Homo sapiens 2,4-dienoyl CoA reductase 1, mitochondrial, mRNA (cDNA clone MGC:132742 IMAGE:8144085), complete cds.BC143669 - Homo sapiens cDNA clone IMAGE:9052183.AK300069 - Homo sapiens cDNA FLJ50204 complete cds, highly similar to 2,4-dienoyl-CoA reductase, mitochondrial precursor (EC 1.3.1.34).L26050 - Human mitochondrial 2,4-dienoyl-CoA reductase mRNA, complete cds.KJ891039 - Synthetic construct Homo sapiens clone ccsbBroadEn_00433 DECR1 gene, encodes complete protein.U49352 - Human liver 2,4-dienoyl-CoA reductase mRNA, complete cds.JD314752 - Sequence 295776 from Patent EP1572962.JD287032 - Sequence 268056 from Patent EP1572962.JD244486 - Sequence 225510 from Patent EP1572962.JD499372 - Sequence 480396 from Patent EP1572962.JD552444 - Sequence 533468 from Patent EP1572962.
Biochemical and Signaling Pathways
Other Names for This Gene
Alternate Gene Symbols: B7Z6B8, DECR, DECR_HUMAN, ENST00000220764.1, ENST00000220764.2, ENST00000220764.3, ENST00000220764.4, ENST00000220764.5, ENST00000220764.6, NM_001359, Q16698, Q2M304, Q93085, SDR18C1, uc317czn.1, uc317czn.2UCSC ID: ENST00000220764.7_10RefSeq Accession: NM_001359.2
Protein: Q16698
(aka DECR_HUMAN)
Gene Model Information
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Methods, Credits, and Use Restrictions
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